Amyotrophic Lateral Sclerosis (ALS): Causes, Symptoms and Neurodegenerative Disease Facts
Category: Science & Technology → Health → Neurological Disorders
Correct terminology: Amyotrophic Lateral Sclerosis (ALS), not “Amylotropic Lateral Sclerosis.”
Key Facts
- ALS is a progressive neurodegenerative disorder.
- It primarily damages motor neurons.
- Motor neurons control voluntary muscle movement.
- Progressive loss of motor neurons causes:
- Muscle weakness
- Muscle wasting
- Difficulty speaking
- Difficulty swallowing
- Difficulty breathing
- Cognitive function is often preserved, although some patients can develop frontotemporal cognitive/behavioural changes.
- ALS is also known as motor neuron disease (MND) in many contexts.
Causes
Most cases are sporadic, while a smaller proportion are familial/genetic.
UPSC Key Pointers
- ALS → Neurodegenerative disease
- Main cells affected → Motor neurons
- Major outcome → Progressive muscle weakness
- Do not confuse ALS with:
- Multiple sclerosis
- Parkinson's disease
- Alzheimer's disease
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